Carnitine Deficiency-induced Cardiomyopathy in a Mouse.
نویسندگان
چکیده
منابع مشابه
Primary Carnitine Deficiency and Cardiomyopathy
Carnitine is essential for the transfer of long-chain fatty acids from the cytosol into mitochondria for subsequent β-oxidation. A lack of carnitine results in impaired energy production from long-chain fatty acids, especially during periods of fasting or stress. Primary carnitine deficiency (PCD) is an autosomal recessive disorder of mitochondrial β-oxidation resulting from defective carnitine...
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ژورنال
عنوان ژورنال: Journal of Toxicologic Pathology
سال: 2000
ISSN: 0914-9198,1881-915X
DOI: 10.1293/tox.13.197